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Ontology Browser

Term:
granulomatosis with polyangiitis (DOID:12132)
Annotations: Rat: (11) Mouse: (10) Human: (12) Chinchilla: (8) Bonobo: (11) Dog: (10) Squirrel: (8) Pig: (11)
Parent Terms Term With Siblings Child Terms
46,XX Sex Reversal with Dysgenesis of Kidneys, Adrenals, and Lungs  
Achenbach syndrome 
Acneiform Eruptions +   
adiaspiromycosis 
AIDS-Associated Nephropathy  
allergic cutaneous vasculitis +   
Alsing Syndrome 
ancylostomiasis +  
angioedema +   
anuria +   
Arnold Stickler Bourne Syndrome 
atheroembolism of kidney 
autoimmune disease of skin and connective tissue +   
autoimmune hemolytic anemia +   
Autoimmune Interstitial Lung, Joint, and Kidney Disease  
Bifid Nose with or without Anorectal And Renal Anomalies  
Birt-Hogg-Dube syndrome  
Blue Diaper Syndrome 
Boudhina Yedes Khiari syndrome 
breast disease +   
bronchiolitis obliterans +   
C syndrome  
CAKUT1  
cercarial dermatitis 
chancroid +  
chronic ulcer of skin +   
Churg-Strauss syndrome  
coenurosis 
Complement Factor H Deficiency  
contagious pustular dermatitis 
Cutaneous Fistula 
cutaneous lupus erythematosus +   
cutis laxa +   
cystic kidney disease +   
Dermal Fibrosis  
dermatitis +   
Dermatoleukodystrophy 
dermatomyositis +   
desquamative interstitial pneumonia  
diabetes insipidus +   
Diabetic Nephropathies  
Dimauro Disease  
dioctophymiasis 
dipetalonemiasis 
Duplication of Eyebrows with Stretchable Skin and Syndactyly 
Ectodermal Dysplasia-Skin Fragility Syndrome  
Eczematous Skin Diseases +   
Elastosis Perforans Serpiginosa 
Elliott Ludman Teebi Syndrome 
endometriosis in scar of skin 
epidermal nevus +   
Erythema +   
erythematosquamous dermatosis 
exanthem +   
extrinsic allergic alveolitis +   
eyelid disease +   
FACES Syndrome 
facial dermatosis +   
Facial Ectodermal Dysplasia  
familial juvenile hyperuricemic nephropathy +   
filariasis +   
Flynn Aird Syndrome 
Foot Diseases +   
Frank-Ter Haar syndrome  
Genetic Skin Diseases +   
Glomerular Diseases +   
Goodpasture syndrome +   
granulomatosis with polyangiitis +   
An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels. (DO)
hair disease +   
hand dermatosis +  
Hantavirus hemorrhagic fever with renal syndrome +   
hemorrhoid +   
Hernandez Fragoso Syndrome 
Herrmann Syndrome 
Hydranencephaly with Renal Aplasia-Dysplasia  
hydronephrosis +   
Hyperoxaluria +   
hypophosphatemic nephrolithiasis/osteoporosis +   
ichthyosis +   
Ichthyosis, Mental Retardation, Dwarfism, and Renal Impairment 
idiopathic interstitial pneumonia +   
Infectious Skin Diseases +   
Infundibulopelvic Dysgenesis 
INTERSTITIAL LUNG AND LIVER DISEASE  
Interstitial Lung Disease, Nephrotic Syndrome, and Epidermolysis Bullosa, Congenital  
Jejunal Atresia with Renal Adysplasia 
Joubert syndrome 5  
Joubert syndrome 6  
Joubert syndrome 9  
juvenile xanthogranuloma 
keratosis +   
kidney cortex disease +  
kidney failure +   
kidney hypertrophy 
Kidney Neoplasms +   
kidney papillary necrosis 
Kimura disease 
Lachiewicz Sibley Syndrome 
Langerhans-cell histiocytosis +   
leg dermatosis 
lipomatosis +   
Lipoprotein Glomerulopathy  
localized scleroderma +   
loiasis 
Lymphedema-Distichiasis Syndrome with Renal Disease and Diabetes Mellitus  
lymphoid interstitial pneumonia 
Macroepiphyseal Dysplasia, McAlister Coe Type 
MASS Syndrome  
mastocytosis +   
Median Cleft Lip, Corpus Callosum, Lipoma, and Skin Polyps 
Mental Retardation, Joint Hypermobility, and Skin Laxity, with or without Metabolic Abnormalities 
Metabolic Skin Diseases +   
Microscopic Polyangiitis  
mongolian spot  
Morgellons Disease 
multicentric reticulohistiocytosis 
multiple cutaneous and mucosal venous malformations  
nail disease +   
necrobiosis lipoidica 
Necrobiotic Disorders +  
Necrolytic Migratory Erythema 
nephritis +   
nephrocalcinosis +   
nephrogenic diabetes insipidus +   
Nephrogenic Fibrosing Dermopathy  
nephrolithiasis +   
nephronophthisis-like nephropathy 1  
Nephropathy with Pretibial Epidermolysis Bullosa and Deafness  
nephrosclerosis +   
NEURODEVELOPMENTAL DISORDER WITH MICROCEPHALY, CATARACTS, AND RENAL ABNORMALITIES  
noninfectious dermatoses of eyelid +  
obstructive nephropathy  
orthostatic proteinuria 
otulipenia  
Papulosquamous Skin Diseases +   
perinephritis 
phaeohyphomycosis +  
photosensitivity disease +   
pigmentation disease +   
pneumoconiosis +   
Premature Atherosclerosis with Deafness, Nephropathy, Diabetes Mellitus, Photomyoclonus, and Degenerative Neurologic Disease 
primary thrombocytopenia +   
proteinuria +   
Prurigo  
Pruritus +   
Pseudoatrophoderma Colli 
pulmonary fibrosis +   
pulmonary sarcoidosis  
pyelitis +   
Radiation Nephropathy  
Radiation Pneumonitis  
Radio Renal Syndrome 
Rajab Interstitial Lung Disease with Brain Calcifications 1  
Rajab Interstitial Lung Disease with Brain Calcifications 2 
reactive cutaneous fibrous lesion +  
renal agenesis +   
renal artery disease +   
renal artery obstruction +   
Renal Dysplasia - Limb Defects Syndrome 
renal fibrosis +   
renal hypertension +   
renal hypoplasia +   
renal infectious disease 
Renal Ischemia  
Renal Nutcracker Syndrome 
renal osteodystrophy  
renal tuberculosis  
Renal Tubular Dysgenesis  
renal tubular transport disease +   
Renal Tubulopathy, Diabetes Mellitus, and Cerebellar Ataxia due to Duplication of Mitochondrial DNA 
rheumatoid arthritis interstitial lung disease 
rosacea +   
Roy Maroteaux Kremp Syndrome 
scalp dermatosis +   
sebaceous gland disease +   
secondary hyperparathyroidism of renal origin 
Selig Benacerraf Greene Syndrome 
Siegler Brewer Carey Syndrome 
Skin Abnormalities +   
skin atrophy 
Skin Neoplasms +   
skin sarcoidosis 
Spastic Paraplegia, Sensorineural Deafness, Mental Retardation, and Progressive Nephropathy 
stricture or kinking of ureter 
strongyloidiasis  
Surfactant Dysfunction  
Surfactant Metabolism Dysfunction, Pulmonary, 1  
Surfactant Metabolism Dysfunction, Pulmonary, 2  
Surfactant Metabolism Dysfunction, Pulmonary, 3  
Surfactant Metabolism Dysfunction, Pulmonary, 5  
sweat gland disease +   
Thrombocytopenia with Elevated Serum Iga and Renal Disease 
Thyrocerebral-Retinal Syndrome 
tyrosinemia type II  
Upton Young Syndrome 
uremia +   
urticaria +   
vascular skin disease +   
verruciform xanthoma of skin 
vesiculobullous skin disease +   
Webb-Dattani Syndrome  
Zellweger syndrome +   

Synonyms
Exact Synonyms: WG ;   Wegener granulomatosis ;   Wegener granulomatosis, formerly ;   Wegener's granulomatosis ;   Wegener's syndrome ;   granulomatosis with polyangiitides ;   necrotizing respiratory granulomatosis
Primary IDs: MESH:D014890
Alternate IDs: OMIM:608710
Xrefs: GARD:7880 ;   ICD10CM:M31.3 ;   ICD9CM:446.4 ;   NCI:C3444
Definition Sources: https://en.wikipedia.org/wiki/Granulomatosis_with_polyangiitis "DO"

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RGD is funded by grant HL64541 from the National Heart, Lung, and Blood Institute on behalf of the NIH.