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Malignant Atrophic Papulosis (DOID:9001237)
Annotations: Rat: (0) Mouse: (0) Human: (0) Chinchilla: (0) Bonobo: (0) Dog: (0) Squirrel: (0) Pig: (0)
Parent Terms Term With Siblings Child Terms
vasculitis +     
angioma serpiginosum +  
arteriosclerosis +   
Arteritis +   
bacillary angiomatosis 
Behcet's disease +   
carotid stenosis +   
central nervous system vasculitis +   
Churg-Strauss syndrome  
Cogan syndrome +   
cryoglobulinemic vasculitis  
Cutis Marmorata Telangiectatica Congenita 
Fibromuscular Dysplasia +  
Gardner-Diamond Syndrome 
Grange Syndrome  
granulomatous angiitis 
Granulomatous Vasculitis  
Henoch-Schoenlein purpura +   
hypersensitivity vasculitis +   
Kawasaki disease  
Leriche Syndrome 
Livedo Reticularis +   
livedoid vasculitis 
Malignant Atrophic Papulosis 
Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.
Megalencephaly Cutis Marmorata Telangiectatica Congenita  
mesenteric vascular occlusion  
Moyamoya disease +   
Nodular Lymphocytic Vasculitis 
Peripheral Arterial Occlusive Disease 1  
phlebitis +   
polyarteritis nodosa +   
Pulmonary Artery Stenosis 
pyoderma gangrenosum +   
renal artery obstruction +   
retinal artery occlusion +   
retinal vasculitis +   
Shwartzman phenomenon  
Sneddon syndrome  
Systemic Vasculitis +   
Takayasu's arteritis  
temporal arteritis +   
thromboangiitis obliterans  
urticaria +   
Vasculitis of the Skin  
Vasculitis, Lymphocytic, Cutaneous Small Vessel 

Exact Synonyms: Degos Disease ;   Degos Syndrome ;   Degos's Malignant Atrophic Papulosis ;   Erythrokeratoderma en cocardes ;   Kohlmeier-Degos Disease ;   Malignant Atrophic Papuloses
Primary IDs: MESH:D054853 ;   RDO:0007690
Definition Sources: MESH:D054853

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RGD is funded by grant HL64541 from the National Heart, Lung, and Blood Institute on behalf of the NIH.